Discussion
- pigmented villonodular synovitis is a slow growing, benign, and locally invasive tumor of the synovium;
- location: most often involves the knee (also in hip, ankle, elbow, etc.);
- always consider PVNS in a younger patient with unexplained hip pain;
- acute episodic attacks of pain and swelling may occur;
- patients may have mechanical symptoms (locking and catching);
- most have hemorrhagic, dark brown synovial fluid;
- biopsy is diagnostic;
- diff dx: rheumatoid arthritis: unlike PVNS, RA tends to affect multiple joints;
- sub-types:
- it usually presents as a monoarticular hemarthrosis, and may exist in a nodular or a diffuse form;
- diffuse form:
- disease may be active or inactive;
- look for peri-articular erosions on radiographs;
- diffuse mass may be present on exam;
- nodular form:
- less common than the diffuse form of the disease;
- does not show the same destructive changes as the diffuse form of PVNS;
- may cause recurrent hemarthrosis and aspirate may be of normal color (may not show classic brown color);
Radiographs
reference: Roentgenographic findings in pigmented villonodular synovitis of the knee.
MRI Findings
- most characteristic feature of PVNS on MRI is the presence of intraarticular nodular masses of low signal intensity on T1, T2-weighted, and proton-density-weighted images;
- diseased synovium and focal masses may be best demonstrated on T2 images, showing up as a void of signal intensity felt due to hemosiderin deposition;
- hypo-intense signal is also seen on T1 images;
- MRI differential diagnosis:
- hemophilic arthropathy
- soft-tissue sarcoma
- fibromatosis
- synovial chondromatosis
- septic arthritis
- inflammatory arthropathies
- hemorrhagic synovitis
- references:
- Magnetic resonance imaging in the diagnosis of aggressive villonodular synovitis.
- The use of magnetic resonance imaging in the diagnosis of pigmented villonodular synovitis.
- The use of MRI to assist in diagnosis of pigmented villonodular synovitis of the knee joint.
- MRI eval and arthroscopic resection of localized pigmented villonodular synovitis of knee.
Histology
- histologic characteristics are similar to GCT of tendon sheath;
- classic cytoarchitecture consists of subsynovial nodular proliferation of large round, polyhedral, or spindle cells with prominent cytoplasm and pale nuclei;
- phagocytic histiocyte-like cells are also present;
- lipid-laden foam cells and multinucleated giant cells are interspersed with hemosiderin-laden cells that resemble lining cells;
- giant cells appear to have phagocytic role;
- findings include deposition of iron, foam cells, or giant cells;
Treatment:
- arthroscopic synovectomy:
- may be indicated for nodular form or for inactive form of diffuse disease;
- some authors stress the importance of a synovectomy of the posterior compartment;
- references:
- radiation therapy:
- Blanco, et al: results of combined partial arthroscopic synovectomy and low-dose xrt in the treatment of diffuse PVNS of the knee;
- PRS of 22 patients with clinical, ultrasonic, and histologically confirmed findings of diffuse PVNS of the knee;
- protocol included anterior (patellofemoral, medial, and lateral) arthroscopic synovectomy and postop RT with a total dose of 2,600 cGy;
- combination therapy was effective in reducing symptoms of pain and edema, and in improving overall function of patients;
- 19 patients (86%) had good or excellent results at an average follow-up of 33 months (range, 26 to 76 months);
- 3 had confirmed recurrence of dz and were treated with repeat arthroscopic synovectomy w/o harmful effects from RT;
- references:
- Blanco, et al: results of combined partial arthroscopic synovectomy and low-dose xrt in the treatment of diffuse PVNS of the knee;
- open synovectomy:
- treatment of choice for patients w/ active form of diffuse disease;
- recurrence rate is relatively high and therefore both anterior and posterior open synovectomy is required;
- total knee arthroplasty:
- indicated for PVNS with joint destructive changes;
- posterior stabilized prosthesis is recommended in order to maximize the exposure as well as the open synovectomy;
- in the report by Hamlin BR, et al (1997), out of 13 patients w/ active diffuse PVNS who underwent TKR, 2 had recurrence
- ref: Total knee arthroplasty in patients who have pigmented villonodular synovitis
References
- Pigmented villonodular synovitis of the wrist and adjacent bones
- Pigmented villonodular synovitis. A retrospective review of affected large joints
- Pigmented villonodular synovitis (giant-cell tumor of the tendon sheath and synovial membrane). A review of eighty-one cases
- Surgical treatment of diffuse pigmented villonodular synovitis of the knee.
- Pigmented villonodular synovitis
- Pigmented villonodular synovitis of synovial joints: clinical, pathologic, and radiologic features
- Pigmented Villonodular Synovitis: Keys to Early Diagnosis
- Treatment of Advanced Primary and Recurrent Diffuse Pigmented Villonodular Synovitis of the Knee
- Localized pigmented villonodular synovitis of the knee
- Pigmented villonodular synovitis about the ankle: a review of the literature and presentation in 10 athletic patients
- Surgical Treatment of Pigmented Villonodular Synovitis of the Hip
- What Affects the Recurrence and Clinical Outcome of Pigmented Villonodular Synovitis?