- is X-linked recessive dystrophy that shares many of the features of DMD, including pseudohypertrophy of muscles;
- main clinical difference is that the course is more protracted;
- patients are usually able to walk as late as early adulthood and often live into their 30s and 40s;
- Lower Extremities:
- equinus deformities & toe-walking are common;
- consider Vulpius heel-cord lengthening, performed in conjunction, if needed, with a posterior tibial-tendon transfer
Current Concepts Review. The Diagnosis and Orthopaedic Treatment of Inherited Muscular Diseases of Childhood.