Developmental Dysplasia of the Hip
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Wheeless' Textbook of Orthopaedics

Hip in Myelomeningocele



- Dislocation of Hip:
    - hip dislocation in children w/ myelomeningocele may either teratological or paralytic (which is due to muscle imbalance);
    - paralytic dislocation:
            - hip dislocation occurs because of paralysis of the hip abductors and extensors w/ unopposed hip flexors and adductors;
            - in the past, hip dislocation was thought to be most common at the L3-L4 level,
                  however, some argue that dislocation more common w/ high level lesions;
                  - note that w/ an L4 lesion there will be paralysis of the gluteus medius and gluteus maximus
                          w/ preservation of the psoas and the adductor longus;
    - if subluxation is not treated, it eventually causes dislocation of hip;
    - dislocated hips do not appear to have any relation to ability to walk and rarely cause pain;
    - asymmetry of the pelvis will adversely affect walking ability;
    - inability to walk is directly related to:
          - level of paralysis;
          - presence of syringomyelia;
          - Arnold-Chiari malformation
          - scoliosis
          - function of the upper extremities;
          - age of patient;

- Treatment Goals:
    - basic premises:
            - painless dislocated hip is preferable to stiff, painful, reduced hip;
            - dislocated hips in the child unable to walk require no treatment;
            - aim of surgery is to maintain ROM & achieve full hip extension;
            - containment of hip is a secondary concern;
    - thoracic or upper lumbar lesion:
            - exam: w/ grade 2 quad function, pt's paralysis level is high lumbar;
            - w/ both hips unstable, most agree no treatment is indicated;
            - anterior hip release for hip flexion contractures may be necessary;
            - attempt to prevent contractures that will interfere w/ walking in a HKAFO during the first ten years of life;
                  - this can usually be accomplished w/ PT & positioning;
                  - thereafter, most of these pts use wheelchair full time;
            - muscle transfers alone usually are not effective in producing stability of
                  hip in children who have lesion at L1 or L2 should not be done;
    - low lumbar lesion:
          - reduction of hips is indicated for prevention of progressive subluxation which will ultimately interfere w/ of walking;
          - w/ L4 or lower lesion, reduce hips and perform varus and or Pemberton osteotomy to avoid future
                  leg length discrepancy or pelvic obliquity;
    - hip flexion contracture:
          - fixed flexion deformity of the hip may interfere w/ fitting of standing frame, parapodium, or reciprocating gait orthosis;

- Indications for Reduction:
    - child who walks;
    - unilateral dislocation;
    - age: one & three years;
    - stable neurological status at L3 or L4;
    - children w/ strong quads &, esp, those w/ functional hamstrings may
            benefit from surgical correction of subluxating or dislocated hips;

- Contra-indications for Reduction:
    - bilateral teratological dislocation;
    - dislocated hips in the child unable to walk require no treatment;

- Soft-tissue procedures seek to balance muscle forces;
            - Sharrard procedure:
                  - involves transfer of iliopsoas to greater trochanter;
                  - alternative procedure: transfer of external oblique muscle combined
                          with adductor tenotomy or transfer of adductors to the ischium;
                  - indications:
                          - lower-level lesion;
                          - no function of abductors & extensors of hip;
                          - good potential for walking;
            - balancing of muscle forces involves a combination of lengthening or transfer of iliopsoas,
                  external oblique, rectus femoris, sartorius, & tensor fasciae latae muscles;
            - tenotomy of iliopsoas & adductor muscles may relieve the muscle balance about the hip,
                  but will severely weaken it;
                  - this results in decreased walking ability and may require extending brace above the hip;

- Osseous procedures seek to correct deficiency of acetabulum as well as
      to correct center the femoral head in the acetabulum;
      - Shelf procedure, Pemberton osteotomy, or Chiari osteotomy may be used for correction of deficiency of the acetabulum;
              - of note, a Salter osteotomy would be a poor choice for a paralytic posterior dislocation, since this
                      type of osteotomy provides anterior coverage at the expense of posterior coverage;
      - femoral osteotomy should be performed to correct rotational & angular
              deformity, with care being taken to avoid too much varus angulation;
              - although it is possible to carry out open reduction and provide temporary stability to the hip with the varus
                      osteotomy, capsule will stretch out w/ redislocation of hip unless muscle forces around hip can be balanced;









The natural history of hip deformity in myelomeningocele.

Walking ability after transplantation of the iliopsoas: A long term follow-up.
      Stillwell A, Menelaus MB:
      J Bone Joint Surg 1984;66B:656.

Effectiveness of muscle transfer in myelomeningocele hips measured by radiographic indices.
      Yngve DA, Lindseth RE:   J Pediatr Orthop 1982;2:121.

Ambulation in patients with myelomeningocele: A multivariate statistical analysis.
      Samuelsson L, Skoog M:   J Pediatr Orthop 1988;8:569-575.

The effect of hip reduction on function in patients with myelomenigocele: Potential gains and
      hazards of surgical treatment.
      E. Feiwell et al. JBJS Vol 60-A. 1978. p 169-173.






Original Text by Clifford R. Wheeless, III, MD.