- Discussion:
- see chondrosarcoma
- also known as extraskeletal myxoid chondrosarcoma;
- it is known also as chordoid sarcoma because of its resemblance to chordoma;
- accounts for < 2 % of all soft-tissue sarcomas;
- tumor usually affects men, in fifth decade of life;
- tumor frequently arises in deep soft tissues, esp of lower extremity and frequently the foot;
- pts usually present w/ gradually enlarging mass, with or without pain;
- prognosis:
- extraskeletal myxoid chondrosarcoma typically behaves as a low-grade sarcoma;
- reported five-year survival rate has ranged from 65 to 85 %;
- Radiographs: neoplasm appears as nodular, radiolucent mass;
- Histology:
- proliferation of ovoid and bipolar cells w/ in prominent myxoid matrix;
- individual tumor cells are surrounded by lacunar spaces, but formation of well-developed hyaline cartilage is uncommon