Ortho-Preferred

Syndactyly: Associated Syndromes


    - Acrosyndactyly;
    - Delta Phalanx;
    - Poland's syndrome:
           - hypoplasia of hand and simple syndactyly of fingers on the same side as the absent pectoral muscles (and other chest wall muscles);
    - Apert's Syndrome:
           - when all digits are joined, as is common in spoon hand of Apert's syndrome (acrocephalosyndactyly), it is important to release border 
                 digits-thumb and small finger-first;
           - remaining 3 joined fingers can be managed by removing middle digit, thus creating a three-fingered hand with a thumb and sufficient
                 skin for closure;
    - Chromosomal Syndromes:
           - trisomy of 13, 18, or 21;
           - deletion of short arm of chromsome 5;
    - Craniofacial Syndromes:
           - Aglossia adactylia
           - Mobius Syndrome
           - Oculomandibulofacial syndrome



Original Text by Clifford R. Wheeless, III, MD.

Last updated by Data Trace Staff on Thursday, September 8, 2011 1:53 pm